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Case Review: Klippel-Feil Syndrome Harvey Levy, DMD, MAGD ACADEMY OF GENERAL DENTISTRY JUNE 27-28, 2013 Klippel-Feil Syndrome Seth W. age 20 Characteristics of KFS short neck low hair line restriction of neck motion congenital fusion of at least two cervical segments. Associated Abnormalities: scoliosis spina bifida anomalies of the kidneys and the ribs cleft palate respiratory problems heart malformations as well as . . . Abnormalities of: head and face, skeleton, sex organs, muscles, brain and spinal cord, arms, legs, and fingers. Seth W., First dental visit at age 5, 1990 Klippel-Feil Syndrome • Heart murmur • Deaf • Patent ductus arteriosis • Hypospadias • Spinal fusion Hospital out-patient OR 1-23-06 Pre-op Dx Treatment Follow-up Special considerations: • Anesthetic risk of Nasal intubation • Multi-disciplinary dental care Tips and tricks Anesthesiologist communicates with Seth via interpreter Seth signs back to anesthesiologist via interpreter Seth leaves pre-op, tells parents “Live Long and Prosper” Old pan: 8-5-98 Pan showing third molars: 11-2-05 In OR getting ready to intubate Preparing for nasal intubation Preparing for nasal intubation Preparing for nasal intubation Preparing for nasal intubation Nasal tube in place Nasal tube and drapes Nasal tube, drapes, throat pack Different Case: Teeth #9, 10 decayed and fractured Teeth #9, 10 palatal view Teeth 9, 10, 19 decayed and fractured Ankyloglossia
