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The Medal Kick Lorem ipsum dolor sit amet consectetuer Case Study: Treatment of Scoliosis with a Wood Cheneau Rigo Orthosis in 10mo patient with Ehlers Danlos Syndrome Ocular Scoliosis Type FKBP-14 Discussion One patient initially fit with 2 WCR orthoses. One bi-valve, one standard anterior opening. The anterior opening was easiest to don and proved best results. After the patient was fit with the WCR she began crawling, pushing her own wheelchair, rolling over and sitting with an upright posture. The patient wore 2 more WCRs (re-fit every 8 weeks due to growth) for a total of 3 WCRs prior to 17 mos of age. Her out of brace curve increased and the patient was referred for Mehta casting. She was then discharged from Mehta casting due to skin breakdown. The curve continued to increase. Significance The patient’s scoliosis is expected to worsen until she reaches skeletal maturity, due to the EDS Ocular Scoliosis Type FKBP-14 diagnosis. Her skin integrity made conservative scoliosis treatment difficult. The WCR orthosis provided a benefit over Mehta casting, because it was removable for skin checks and may reduce the risk of skin ulceration in patients with this form of EDS. If conservative treatment of infantile scoliosis with WCR orthoses can be tolerated better than Mehta casting, surgical interventions can be prolonged until later in life. § Ehlers-Danlos Syndrome is a genetically heterogeneous group of conditions of which the main features are skin hyperextensibility, joint hypermobility, easy bruising and generalized connective tissue fragility. § Advancing infantile scoliosis of a 38° Curve progressed over a 6month period led to a referral for external bracing to delay operative management. § Skin welts and tearing are a concern for the parents. The skin could tolerate the correction rotational forces built into the plastic form of the Wood Cheneau Rigo. § The patient was able to begin independent locomotion with her wheelchair with her Wood Cheneau Rigo Scoliosis Orthosis on. § 23 hour WCR wear time was followed easily as the patient was easier to carry. Conclusion § Ultimately Mehta casting was applied to this patient because the out of brace curve progression was not halted by the Wood Cheneau Rigo Scoliosis (WCR) TLSO. However, the opportunity for removal of the WCR to perform skin checks while still reducing the curve was beneficial. Marlies Beerli Cabell, CPO Ability Prosthetics and Orthotics, Inc. Initial Xray: Initial Evaluation on 10/23/2017. 38° T8 apical vertebrae. 11/10/2017 2/12/2018 5/14/2018 Able to complete independent locomotion with upper extremity full ROM. 10 month old. 17.7 lbs 14 mos 22lbs 30.5inches Introduction This 10mo female patient with EDS Ocular Scoliosis Type FKBP-14 presented with a spinal curve of 38°. She was referred for orthotic management with the Wood Cheneau Rigo (WCR) orthosis instead of Mehta casting, due to skin integrity concerns and parents’ desire to avoid anesthesia. The WCR orthosis provides three-dimensional correction and has significant pressure and expansion areas built into the brace for spinal elongation and derotation. Initial Evaluation on 10/23/2017. November 2018 removal of the Mehta Casting.
