DIDMOD SyndromeDIDMOD Syndrome
Dr Faiza QariDr Faiza Qari
DMDM
Insulin , 3 times /day Insulin , 3 times /day
DIDI
DDAVP nasal spray DDAVP nasal spray
CIC CatheterCIC Catheter
Diagnosis Number of patients Percentage
Urinary system Urinary system anomaliesanomalies
PUV PUV
VURVUR
Renal DysplasiaRenal Dysplasia
Other anomalies Other anomalies
3333
1111
1111
88
3 3
50%50%
17%17%
17%17%
12%12%
4.5% 4.5%
Hereditary conditions:Hereditary conditions:
Congenital nephroticsCongenital nephrotics
ARPKDARPKD
FHHNCFHHNC
Cystinosis Cystinosis
88
33
22
22
1 1
12%12%
4.5%4.5%
3%3%
3%3%
1.5% 1.5%
Neurogenic bladderNeurogenic bladder
Spina bifida or sacral Spina bifida or sacral agenesisagenesis
Idiopathic Idiopathic
1313
99
4 4
19.6%19.6%
13.6%13.6%
6% 6%
GlomerularGlomerular
SRNSSRNS
RPGNRPGN
99
55
44
13.6%13.6%
7.5%7.5%
6%6%
Cortical necrosisCortical necrosis Dr Jamella QariDr Jamella Qari
11 1.5%1.5%
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