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Paediatrics in Picture

Date post: 03-Jun-2018
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PAEDI A TRICS IN PICTURE DR SANA BUSHRA
Transcript
Page 1: Paediatrics in Picture

8/12/2019 Paediatrics in Picture

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PAEDIATRICS IN PICTURE

DR SANA BUSHRA

Page 2: Paediatrics in Picture

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STATION 1

• Identify the spot

• How many grades does

this condition have

• Name 3 diseases having

this condition

Page 3: Paediatrics in Picture

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ANSWER

• a)Clubbing

• b)Four grades

• Grade 1 fluctuation and softening of the nail bed

•Grade 2 obliteration of the normal angle between nailand nail bed

• Grade 3 convexity of the nail ; drum stick appearance

• Grade 4 broadened terminal pulp of the digit

• C) I ) tetralogy of fallot

•   ii) celiac disease

•   iii) cystic fibrosis

Page 4: Paediatrics in Picture

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STATION 2

• Identify

• Give five causes of this

condition

Page 5: Paediatrics in Picture

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ANSWER

• White pupillary reflex

• 1 Post infection congenital rubella

2 Galactosemia• 3 Retinoblastoma

• 4 Coat’s disease 

• 5 Wilson disease

Page 6: Paediatrics in Picture

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STATION 3

• Name the spots

• Give ten causes

Page 7: Paediatrics in Picture

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ANSWER

• Café –au-lait spots

• 1 neurofibromatosis type 1 and 2

• 2 McCune Albright syndrome

• 3 ataxia telangiectasia

• 4 fanconi anemia• 5 Russell-silver syndrome

• 6 Tuberous sclerosis

• 7 Gaucher disease

• 8 Chediak – Higashi syndrome• 9 Turner syndrome

• 10 Proteus syndrome

Page 8: Paediatrics in Picture

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STATION 4

• Name the disease

• Name 10 complications

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ANSWER

• Measles

• 1 Giant cell pneumonia

• 2 Croup

• 3 Acute otitis media

• 4 activation of pulmonary TB• 5 diarrhea and vomiting

• 6 encephalitis

• 7 myocarditis

• 8 appendicitis• 9 hemmorraghic measles

• 10 subacute sclerosing panencephalitis

Page 10: Paediatrics in Picture

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STATION 5

• This chair has received

the attention of a 3

years old boy

• What is the diagnosis• Treatment

Page 11: Paediatrics in Picture

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ANSWER

• Pica

• Iron and calcium supplementation

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STATION 6

• Describe three features

shown in the picture

• What is the inheritance

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ANSWER

• 1 Depressed nasal bridge

• 2 Prominent maxilla

3 Prominent teeth• Inherited as autosomal recessive

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STATION 7

• Name the sign

• Name the condition

• Name an associated

syndrome

Page 15: Paediatrics in Picture

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ANSWER

• Double bubble sign

• Duodenal atresia

Down syndrome

Page 16: Paediatrics in Picture

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STATION 8

• Name the associated

lower limb abnormality

• What should the

mother have taken toavoid this

Page 17: Paediatrics in Picture

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ANSWER

• Pes cavus ( club feet )

• Folic acid

Page 18: Paediatrics in Picture

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STATION 9

• What do you see

• Give five differential

diagnosis

Page 19: Paediatrics in Picture

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ANSWER

• Periorbital bruising

• 1 leukemia

2 neuroblastoma ( results in raccoon eyes)• 3 basal skull fracture

• 4 bleeding disorder such as haemophilia

• 5 non accidental injury

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STATION 10

• This is an x ray of a 4year old boy whopresented with coarsefacies ,

hepatosplenomegalyand short stature

• Name the x ray findingshown

• Name four other x rayfindings

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ANSWER

• Bullet shaped metacarpals

• 1 oar shaped ribs

2 j shaped sella turcica• 3 beaking of the vertebra

• 4 thickened calvarium


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