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Sllavko K. Kallfa
Radiological Signs
Shnja Radiologjike)
Prmbledhje Artikujsh nga
Radiopaedia.org
9
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weapon and munition inspired signs
cannonball metastases..........................f.3
dagger sign........................................................... f.7
panzerherz(armour heart)..f.19
saber-sheath trachea............................ .f.20
Scimitar syndrome.................................. f.23
target sign............................................................ f.35
http://radiopaedia.org/articles/weapon-and-munition-inspired-signshttp://radiopaedia.org/articles/cannonball-metastases-1http://radiopaedia.org/articles/cannonball-metastases-1http://radiopaedia.org/articles/dagger-signhttp://radiopaedia.org/articles/dagger-signhttp://radiopaedia.org/articles/panzerherz-1http://radiopaedia.org/articles/panzerherz-1http://radiopaedia.org/articles/saber-sheath-tracheahttp://radiopaedia.org/articles/saber-sheath-tracheahttp://radiopaedia.org/articles/scimitar-syndromehttp://radiopaedia.org/articles/scimitar-syndromehttp://radiopaedia.org/articles/bulls-eye-sign-generalhttp://radiopaedia.org/articles/bulls-eye-sign-generalhttp://radiopaedia.org/articles/bulls-eye-sign-generalhttp://radiopaedia.org/articles/scimitar-syndromehttp://radiopaedia.org/articles/saber-sheath-tracheahttp://radiopaedia.org/articles/panzerherz-1http://radiopaedia.org/articles/dagger-signhttp://radiopaedia.org/articles/cannonball-metastases-1http://radiopaedia.org/articles/weapon-and-munition-inspired-signs8/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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Cannonball metastases
Dr Henry KnipeandDr Ian Bickleet al.
Cannonball metastasesrefer to large, well circumscribed, round metastases to the lung thatappear like cannonballs.
Metastases with such an appearance are classically fromrenal cell carcinomaorchoriocarcinoma,and less commonly from an alternative primary tumour, such as prostate
cancer,synovial sarcomaorendometrial carcinoma.
The French term "envole de ballons" which translates to "balloons release" is also used to
describe this same appearance.
References
1. Arkless R. RENAL CARCINOMA: HOW IT METASTASIZES. Radiology. 1996;84:
496-501.Pubmed citation
Synonyms & Alternative Spellings
Synonyms or Alternative Spelling Include in Listings?
Cannonball pulmonary metastases
Cannonball metastasis
Cannonball lung metastases
Cannon-ball metastases
Balloons release appearance
http://radiopaedia.org/users/henryknipehttp://radiopaedia.org/users/henryknipehttp://radiopaedia.org/users/clonvarahttp://radiopaedia.org/users/clonvarahttp://radiopaedia.org/users/clonvarahttp://radiopaedia.org/articles/renal-cell-carcinoma-1http://radiopaedia.org/articles/renal-cell-carcinoma-1http://radiopaedia.org/articles/renal-cell-carcinoma-1http://radiopaedia.org/articles/choriocarcinomahttp://radiopaedia.org/articles/choriocarcinomahttp://radiopaedia.org/articles/synovial-sarcomahttp://radiopaedia.org/articles/synovial-sarcomahttp://radiopaedia.org/articles/synovial-sarcomahttp://radiopaedia.org/articles/endometrial-carcinomahttp://radiopaedia.org/articles/endometrial-carcinomahttp://radiopaedia.org/articles/endometrial-carcinomahttp://www.ncbi.nlm.nih.gov/pubmed/14280724http://www.ncbi.nlm.nih.gov/pubmed/14280724http://www.ncbi.nlm.nih.gov/pubmed/14280724http://www.ncbi.nlm.nih.gov/pubmed/14280724http://radiopaedia.org/articles/endometrial-carcinomahttp://radiopaedia.org/articles/synovial-sarcomahttp://radiopaedia.org/articles/choriocarcinomahttp://radiopaedia.org/articles/renal-cell-carcinoma-1http://radiopaedia.org/users/clonvarahttp://radiopaedia.org/users/henryknipe8/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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From the case:Renal cell carcinoma with pulmonary metastases
Modality: X-ray
http://radiopaedia.org/cases/renal-cell-carcinoma-with-pulmonary-metastaseshttp://radiopaedia.org/cases/renal-cell-carcinoma-with-pulmonary-metastaseshttp://radiopaedia.org/cases/renal-cell-carcinoma-with-pulmonary-metastaseshttp://radiopaedia.org/cases/renal-cell-carcinoma-with-pulmonary-metastases8/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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From the case:Cannon ball metastases - from synovial sarcoma
Modality: CT
http://radiopaedia.org/cases/cannon-ball-metastases-from-synovial-sarcomahttp://radiopaedia.org/cases/cannon-ball-metastases-from-synovial-sarcomahttp://radiopaedia.org/cases/cannon-ball-metastases-from-synovial-sarcomahttp://radiopaedia.org/cases/cannon-ball-metastases-from-synovial-sarcoma8/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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Frontal
Cannon-ball metastasis From the case:Lung metastases
Modality: X-ray
http://radiopaedia.org/cases/lung-metastaseshttp://radiopaedia.org/cases/lung-metastaseshttp://radiopaedia.org/cases/lung-metastaseshttp://radiopaedia.org/cases/lung-metastases8/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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Dagger sign
Dr Henry KnipeandDr Frank Gaillardet al.
The dagger signis a radiographic feature seen inankylosing spondylitisas single centralradiodense line on frontal radiographs related to ossification of supraspinous and interspinousligaments.
o
References
1. Bone and joint imaging. Donald Resnick, Mark J. Kransdorf. Philadelphia, Pa. :
Elsevier Saunders, c2005.ISBN:0721602703(find it at amazon.com)
Synonyms & Alternative Spellings
Synonyms or Alternative Spelling Include in Listings?
The dagger sign
http://radiopaedia.org/users/henryknipehttp://radiopaedia.org/users/henryknipehttp://radiopaedia.org/users/frankhttp://radiopaedia.org/users/frankhttp://radiopaedia.org/users/frankhttp://radiopaedia.org/articles/ankylosing-spondylitishttp://radiopaedia.org/articles/ankylosing-spondylitishttp://radiopaedia.org/articles/ankylosing-spondylitishttp://www.worldcat.org/wcpa/isbn/0721602703http://www.worldcat.org/wcpa/isbn/0721602703http://www.amazon.com/gp/product/0721602703?ie=UTF8&tag=radiopaediaor-20&linkCode=as2&camp=1789&creative=9325&creativeASIN=0721602703http://www.amazon.com/gp/product/0721602703?ie=UTF8&tag=radiopaediaor-20&linkCode=as2&camp=1789&creative=9325&creativeASIN=0721602703http://www.amazon.com/gp/product/0721602703?ie=UTF8&tag=radiopaediaor-20&linkCode=as2&camp=1789&creative=9325&creativeASIN=0721602703http://www.amazon.com/gp/product/0721602703?ie=UTF8&tag=radiopaediaor-20&linkCode=as2&camp=1789&creative=9325&creativeASIN=0721602703http://www.worldcat.org/wcpa/isbn/0721602703http://radiopaedia.org/articles/missing?article%5Btitle%5D=missinghttp://radiopaedia.org/articles/missing?article%5Btitle%5D=missinghttp://radiopaedia.org/articles/ankylosing-spondylitishttp://radiopaedia.org/users/frankhttp://radiopaedia.org/users/henryknipe8/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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Dagger Photo by Jrgen Adam Holen. This file is licensed under Creative Commons Attribution 1.0
license
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Dagger sign of ankylosing spondylitis
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From the case:Ankylosing spondylitis of the
lumbar spine
Modality: X-ray
http://radiopaedia.org/cases/ank-spond-lumbarjpghttp://radiopaedia.org/cases/ank-spond-lumbarjpghttp://radiopaedia.org/cases/ank-spond-lumbarjpghttp://radiopaedia.org/cases/ank-spond-lumbarjpghttp://radiopaedia.org/cases/ank-spond-lumbarjpghttp://radiopaedia.org/cases/ank-spond-lumbarjpg8/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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From the case:
Dagger sign in ankylosing spondylitis
Modality: X-ray
http://radiopaedia.org/cases/dagger-sign-in-ankylosing-spondylitishttp://radiopaedia.org/cases/dagger-sign-in-ankylosing-spondylitishttp://radiopaedia.org/cases/dagger-sign-in-ankylosing-spondylitis8/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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From the case:
Ankylosing spondylitis with bamboo spine and dagger sign
Modality: X-r
http://radiopaedia.org/cases/ankylosing-spondylitis-with-bamboo-spine-and-dagger-signhttp://radiopaedia.org/cases/ankylosing-spondylitis-with-bamboo-spine-and-dagger-signhttp://radiopaedia.org/cases/ankylosing-spondylitis-with-bamboo-spine-and-dagger-sign8/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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From the case:
Ankylosing spondylitis - with dagger sign
Modality: CT
http://radiopaedia.org/cases/ankylosing-spondylitis-with-dagger-signhttp://radiopaedia.org/cases/ankylosing-spondylitis-with-dagger-signhttp://radiopaedia.org/cases/ankylosing-spondylitis-with-dagger-sign8/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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From the case:
Ankylosing spondylitis
Modality: X-ray
http://radiopaedia.org/cases/ankylosing-spondylitis-19http://radiopaedia.org/cases/ankylosing-spondylitis-19http://radiopaedia.org/cases/ankylosing-spondylitis-198/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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From the case:
Ankylosing spondylitis
Modality: X-ray
http://radiopaedia.org/cases/ankylosing-spondylitis-19http://radiopaedia.org/cases/ankylosing-spondylitis-19http://radiopaedia.org/cases/ankylosing-spondylitis-198/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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From the case:Ankylosing spondilitis
Modality: Annotated image
http://radiopaedia.org/cases/ankylosing-spondilitishttp://radiopaedia.org/cases/ankylosing-spondilitishttp://radiopaedia.org/cases/ankylosing-spondilitishttp://radiopaedia.org/cases/ankylosing-spondilitis8/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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From the case:Ankylosing spondilitis
Modality: Annotated image
http://radiopaedia.org/cases/ankylosing-spondilitishttp://radiopaedia.org/cases/ankylosing-spondilitishttp://radiopaedia.org/cases/ankylosing-spondilitishttp://radiopaedia.org/cases/ankylosing-spondilitis8/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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Panzerherz
Dr Yuranga WeerakkodyandDr Ian Bickleet al.
Panzerherz(or armoured heart) is a term used to describe the appearance of the heart incalcified constrictivepericarditis.
Thepericardiumbecomes circumferentially thickened with calcification, limiting the ability ofthe heart to contract. The rim of dense calcification describes how the heart is "armoured", in the
manner a military vehicle is.
The calcification is a generic response to a number of potential insults causingconstrictive
pericarditisincluding:
tuberculosis
viral infections trauma
radiation treatment
References
1. Dewey M, Eddicks S, Hamm B. Images in cardiology: Armoured heart. Heart. 2005;91
(10): 1256.doi:10.1136/hrt.2005.060616-Free text at pubmed-Pubmed citation 2. Eastman G, Wald C. Getting Started in Clinical Radiology: From Image to Diagnosis.
TIS. ISBN:B005NA3D1U.Read it at Google Books-Find it at Amazon
Synonyms & Alternative Spellings
Synonyms or Alternative Spelling Include in Listings?
Porcelin heart
Armoured heart
Armored heart Armour-plated heart
Armor-plated heart
http://radiopaedia.org/users/weer06http://radiopaedia.org/users/weer06http://radiopaedia.org/users/clonvarahttp://radiopaedia.org/users/clonvarahttp://radiopaedia.org/users/clonvarahttp://radiopaedia.org/articles/constrictive-pericarditishttp://radiopaedia.org/articles/constrictive-pericarditishttp://radiopaedia.org/articles/constrictive-pericarditishttp://radiopaedia.org/articles/pericardiumhttp://radiopaedia.org/articles/pericardiumhttp://radiopaedia.org/articles/pericardiumhttp://radiopaedia.org/articles/constrictive-pericarditishttp://radiopaedia.org/articles/constrictive-pericarditishttp://radiopaedia.org/articles/constrictive-pericarditishttp://radiopaedia.org/articles/constrictive-pericarditishttp://radiopaedia.org/articles/tuberculosishttp://radiopaedia.org/articles/tuberculosishttp://dx.doi.org/10.1136/hrt.2005.060616http://dx.doi.org/10.1136/hrt.2005.060616http://dx.doi.org/10.1136/hrt.2005.060616http://www.ncbi.nlm.nih.gov/pmc/articles/PMC1769117http://www.ncbi.nlm.nih.gov/pmc/articles/PMC1769117http://www.ncbi.nlm.nih.gov/pmc/articles/PMC1769117http://www.ncbi.nlm.nih.gov/pubmed/16162604http://www.ncbi.nlm.nih.gov/pubmed/16162604http://www.ncbi.nlm.nih.gov/pubmed/16162604http://books.google.com/books?vid=ISBNB005NA3D1Uhttp://books.google.com/books?vid=ISBNB005NA3D1Uhttp://books.google.com/books?vid=ISBNB005NA3D1Uhttp://www.amazon.com/gp/product/B005NA3D1Uhttp://www.amazon.com/gp/product/B005NA3D1Uhttp://www.amazon.com/gp/product/B005NA3D1Uhttp://www.amazon.com/gp/product/B005NA3D1Uhttp://books.google.com/books?vid=ISBNB005NA3D1Uhttp://www.ncbi.nlm.nih.gov/pubmed/16162604http://www.ncbi.nlm.nih.gov/pmc/articles/PMC1769117http://dx.doi.org/10.1136/hrt.2005.060616http://radiopaedia.org/articles/tuberculosishttp://radiopaedia.org/articles/constrictive-pericarditishttp://radiopaedia.org/articles/constrictive-pericarditishttp://radiopaedia.org/articles/pericardiumhttp://radiopaedia.org/articles/constrictive-pericarditishttp://radiopaedia.org/users/clonvarahttp://radiopaedia.org/users/weer068/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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Saber sheath trachea
Dr Henry KnipeandDr Frank Gaillardet al.
Saber-sheath trachea refers to diffuse coronal narrowing of the intra-thoracic portion of thetrachea with concomitant widening of the sagittal diameter. It is not uncommon and ispathognomonic forchronic obstructive pulmonary disease (COPD)
1.
The sagittal:coronal diameter is over 2:12and the extra-thoracic portion of the trachea is not
narrowed.
Radiographic features
Marked decrease in the coronal diameter of the intra-thoracic trachea associated with an increase
in its sagittal diameter.
CT
Additional features may include:
inward bowing or displacement of the lateral tracheal walls as a result of cartilageweakness
mild intra-thoracic tracheal wall thickening
ossification of tracheal rings
during forceful expiration, there may be further inward bowing
References
1. Marom EM, Goodman PC, Mcadams HP. Diffuse abnormalities of the trachea and
main bronchi. AJR Am J Roentgenol. 2001;176 (3): 713-7.AJR Am J Roentgenol (fulltext)-Pubmed citation
2. Webb EM, Elicker BM, Webb WR. Using CT to diagnose nonneoplastic tracheal
abnormalities: appearance of the tracheal wall. AJR Am J Roentgenol. 2000;174 (5):
1315-21.AJR Am J Roentgenol (full text)-Pubmed citation
3. Ciccarese F, Poerio A, Stagni S et -al. Saber-sheath trachea as a marker of severe
airflow obstruction in chronic obstructive pulmonary disease. Radiol Med. 2014;119 (2):90-6.doi:10.1007/s11547-013-0318-3-Pubmed citation
Synonyms & Alternative Spellings
Synonyms or Alternative Spelling Include in Listings?
Saber sheath trachea
http://radiopaedia.org/users/henryknipehttp://radiopaedia.org/users/henryknipehttp://radiopaedia.org/users/frankhttp://radiopaedia.org/users/frankhttp://radiopaedia.org/users/frankhttp://radiopaedia.org/articles/chronic-obstructive-pulmonary-disease-1http://radiopaedia.org/articles/chronic-obstructive-pulmonary-disease-1http://radiopaedia.org/articles/chronic-obstructive-pulmonary-disease-1http://www.ajronline.org/content/176/3/713.fullhttp://www.ajronline.org/content/176/3/713.fullhttp://www.ajronline.org/content/176/3/713.fullhttp://www.ajronline.org/content/176/3/713.fullhttp://www.ncbi.nlm.nih.gov/pubmed/11222211http://www.ncbi.nlm.nih.gov/pubmed/11222211http://www.ncbi.nlm.nih.gov/pubmed/11222211http://www.ajronline.org/content/174/5/1315.fullhttp://www.ajronline.org/content/174/5/1315.fullhttp://www.ajronline.org/content/174/5/1315.fullhttp://www.ncbi.nlm.nih.gov/pubmed/10789785http://www.ncbi.nlm.nih.gov/pubmed/10789785http://www.ncbi.nlm.nih.gov/pubmed/10789785http://dx.doi.org/10.1007/s11547-013-0318-3http://dx.doi.org/10.1007/s11547-013-0318-3http://dx.doi.org/10.1007/s11547-013-0318-3http://www.ncbi.nlm.nih.gov/pubmed/24297576http://www.ncbi.nlm.nih.gov/pubmed/24297576http://www.ncbi.nlm.nih.gov/pubmed/24297576http://www.ncbi.nlm.nih.gov/pubmed/24297576http://dx.doi.org/10.1007/s11547-013-0318-3http://www.ncbi.nlm.nih.gov/pubmed/10789785http://www.ajronline.org/content/174/5/1315.fullhttp://www.ncbi.nlm.nih.gov/pubmed/11222211http://www.ajronline.org/content/176/3/713.fullhttp://www.ajronline.org/content/176/3/713.fullhttp://radiopaedia.org/articles/chronic-obstructive-pulmonary-disease-1http://radiopaedia.org/users/frankhttp://radiopaedia.org/users/henryknipe8/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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From
the case:Saber sheath trachea
Modality: X-ray
http://radiopaedia.org/cases/saber-sheath-tracheahttp://radiopaedia.org/cases/saber-sheath-tracheahttp://radiopaedia.org/cases/saber-sheath-tracheahttp://radiopaedia.org/cases/saber-sheath-trachea8/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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Scimitar syndrome
Dr Yuranga WeerakkodyandDr Frank Gaillardet al.
Scimitar syndrome(also known as pulmonary venolobar syndrome orhypogenetic lungsyndrome)4
is characterised by a hypoplastic lung that is drained by an anomalous vein into thesystemic venous system. It is a type ofpartial anomalous pulmonary venous return.
Pathology
It is essentially a combination ofpulmonary hypoplasiaandpartial anomalous pulmonary venous
return(PAPVR).It almost exclusively occurs on the right side.
Haemodynamically, there is an acyanotic left to right shunt. The anomalous vein usually drains
into
inferior vena cava -most common
right atrium
portal vein
The lung is frequently perfused by theaorta,but thebronchial treeis still connected and thus the
lung is not sequestered.
Associations
congenital heart disease (e.g.ASD,VSD,tetralogy of Fallot,PDA)
ipsilateral diaphragmatic anomalies (e.g. accessory diaphragm,diaphragmatic hernia)
localised bronchiectasis
horseshoe lung
vertebral anomalies (e.g.hemivertebrae4)
genitourinary tract abnormalities4
Radiographic features
The diagnosis is made by transthoracic or transesophageal echocardiography, angiography, or by
CT or MR angiography.
Plain film
Chest radiographic findings are that of a small lung with ipsilateral mediastinal shift, and in one
third of cases the anomalous draining vein may be seen as a tubular structure paralleling the right
heart border in the shape of a Turkish sword (scimitar). The right heart border maybe blurred.
Complications
http://radiopaedia.org/users/weer06http://radiopaedia.org/users/weer06http://radiopaedia.org/users/frankhttp://radiopaedia.org/users/frankhttp://radiopaedia.org/users/frankhttp://radiopaedia.org/articles/pulmonary-anomalous-pulmonary-venous-connectionhttp://radiopaedia.org/articles/pulmonary-anomalous-pulmonary-venous-connectionhttp://radiopaedia.org/articles/pulmonary-anomalous-pulmonary-venous-connectionhttp://radiopaedia.org/articles/pulmonary-hypoplasiahttp://radiopaedia.org/articles/pulmonary-hypoplasiahttp://radiopaedia.org/articles/pulmonary-hypoplasiahttp://radiopaedia.org/articles/pulmonary-anomalous-pulmonary-venous-connectionhttp://radiopaedia.org/articles/pulmonary-anomalous-pulmonary-venous-connectionhttp://radiopaedia.org/articles/pulmonary-anomalous-pulmonary-venous-connectionhttp://radiopaedia.org/articles/pulmonary-anomalous-pulmonary-venous-connectionhttp://radiopaedia.org/articles/missing?article%5Btitle%5D=partial-anomalous-pulmonary-venous-returnhttp://radiopaedia.org/articles/missing?article%5Btitle%5D=partial-anomalous-pulmonary-venous-returnhttp://radiopaedia.org/articles/inferior-vena-cava-1http://radiopaedia.org/articles/inferior-vena-cava-1http://radiopaedia.org/articles/missing?article%5Btitle%5D=right-atriumhttp://radiopaedia.org/articles/missing?article%5Btitle%5D=right-atriumhttp://radiopaedia.org/articles/portal-veinhttp://radiopaedia.org/articles/portal-veinhttp://radiopaedia.org/articles/aortahttp://radiopaedia.org/articles/aortahttp://radiopaedia.org/articles/aortahttp://radiopaedia.org/articles/missing?article%5Btitle%5D=bronchial-treehttp://radiopaedia.org/articles/missing?article%5Btitle%5D=bronchial-treehttp://radiopaedia.org/articles/missing?article%5Btitle%5D=bronchial-treehttp://radiopaedia.org/articles/congenital-cardiovascular-anomalieshttp://radiopaedia.org/articles/congenital-cardiovascular-anomalieshttp://radiopaedia.org/articles/atrial-septal-defect-2http://radiopaedia.org/articles/atrial-septal-defect-2http://radiopaedia.org/articles/atrial-septal-defect-2http://radiopaedia.org/articles/ventricular-septal-defect-1http://radiopaedia.org/articles/ventricular-septal-defect-1http://radiopaedia.org/articles/ventricular-septal-defect-1http://radiopaedia.org/articles/tetralogy-of-fallothttp://radiopaedia.org/articles/tetralogy-of-fallothttp://radiopaedia.org/articles/tetralogy-of-fallothttp://radiopaedia.org/articles/patent-ductus-arteriosushttp://radiopaedia.org/articles/patent-ductus-arteriosushttp://radiopaedia.org/articles/patent-ductus-arteriosushttp://radiopaedia.org/articles/diaphragmatic-herniahttp://radiopaedia.org/articles/diaphragmatic-herniahttp://radiopaedia.org/articles/diaphragmatic-herniahttp://radiopaedia.org/articles/horseshoe-lunghttp://radiopaedia.org/articles/horseshoe-lunghttp://radiopaedia.org/articles/hemivertebrahttp://radiopaedia.org/articles/hemivertebrahttp://radiopaedia.org/articles/hemivertebrahttp://radiopaedia.org/articles/hemivertebrahttp://radiopaedia.org/articles/horseshoe-lunghttp://radiopaedia.org/articles/diaphragmatic-herniahttp://radiopaedia.org/articles/patent-ductus-arteriosushttp://radiopaedia.org/articles/tetralogy-of-fallothttp://radiopaedia.org/articles/ventricular-septal-defect-1http://radiopaedia.org/articles/atrial-septal-defect-2http://radiopaedia.org/articles/congenital-cardiovascular-anomalieshttp://radiopaedia.org/articles/missing?article%5Btitle%5D=bronchial-treehttp://radiopaedia.org/articles/aortahttp://radiopaedia.org/articles/portal-veinhttp://radiopaedia.org/articles/missing?article%5Btitle%5D=right-atriumhttp://radiopaedia.org/articles/inferior-vena-cava-1http://radiopaedia.org/articles/missing?article%5Btitle%5D=partial-anomalous-pulmonary-venous-returnhttp://radiopaedia.org/articles/pulmonary-anomalous-pulmonary-venous-connectionhttp://radiopaedia.org/articles/pulmonary-anomalous-pulmonary-venous-connectionhttp://radiopaedia.org/articles/pulmonary-hypoplasiahttp://radiopaedia.org/articles/pulmonary-anomalous-pulmonary-venous-connectionhttp://radiopaedia.org/users/frankhttp://radiopaedia.org/users/weer068/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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A potential complication that could develop is development or pulmonary hypertension an
Eisenmenger physiology.
Treatment
Surgical correction should be considered in the presence of significant left to right shunting andpulmonary hypertension.This involves creation of an inter-atrial baffle to redirect the pulmonaryvenous return into theleft atrium.Alternatively, the anomalous vein can be re-implanted directly
into the left atrium.
Etymology
The term was first given by C A Neillet al in 19605.
Differential diagnosis
General imaging differential considerations include
pulmonary sequestration
right middle lobe atelectasis(on AP plain film)
unilateral absence of pulmonary artery (UAPA)
References
1. Dahnert WF. Radiology Review Manual. (2011) ISBN:1609139437.Read it at Google
Books-Find it at Amazon 2. Melduni RM, Mookadam F, Mulligan ME. Scimitar syndrome: another one for the
radiologists. Radiology. 2006;241 (2): 629.doi:10.1148/radiol.2412051952-Pubmed
citation
2. Olson MA, Becker GJ. The Scimitar syndrome: CT findings in partial anomalouspulmonary venous return. Radiology. 1986;159 (1): 25-6.Radiology (citation)-Pubmed
citation
4. Berrocal T, Madrid C, Novo S et-al. Congenital anomalies of the tracheobronchial tree,lung, and mediastinum: embryology, radiology, and pathology. Radiographics. 24 (1):
e17.doi:10.1148/rg.e17-Pubmed citation
5. Schramel FM, Westermann CJ, Knaepen PJ et-al. The scimitar syndrome: clinical
spectrum and surgical treatment. Eur. Respir. J. 1995;8 (2): 196-201.Eur. Respir. J. (link)-Pubmed citation
6. Baskar karthekeyan R, Saldanha R, Sahadevan MR et-al. Scimitar syndrome:
experience with 6 patients. Asian Cardiovasc Thorac Ann. 2009;17 (3): 266-71.doi:10.1177/0218492309104750-Pubmed citation
7. Woodring JH, Howard TA, Kanga JF. Congenital pulmonary venolobar syndrome
revisited. Radiographics. 1994;14 (2): 349-69.doi:10.1148/radiographics.14.2.8190958-
Pubmed citation
http://radiopaedia.org/articles/missing?article%5Btitle%5D=eisenmenger-syndromehttp://radiopaedia.org/articles/missing?article%5Btitle%5D=eisenmenger-syndromehttp://radiopaedia.org/articles/pulmonary-hypertensionhttp://radiopaedia.org/articles/pulmonary-hypertensionhttp://radiopaedia.org/articles/missing?article%5Btitle%5D=left-atriumhttp://radiopaedia.org/articles/missing?article%5Btitle%5D=left-atriumhttp://radiopaedia.org/articles/missing?article%5Btitle%5D=left-atriumhttp://radiopaedia.org/articles/pulmonary_sequestrationhttp://radiopaedia.org/articles/pulmonary_sequestrationhttp://radiopaedia.org/articles/right-middle-lobe-atelectasishttp://radiopaedia.org/articles/right-middle-lobe-atelectasishttp://radiopaedia.org/articles/missing?article%5Btitle%5D=unilateral-absence-of-pulmonary-artery-uapahttp://radiopaedia.org/articles/missing?article%5Btitle%5D=unilateral-absence-of-pulmonary-artery-uapahttp://books.google.com/books?vid=ISBN1609139437http://books.google.com/books?vid=ISBN1609139437http://books.google.com/books?vid=ISBN1609139437http://books.google.com/books?vid=ISBN1609139437http://www.amazon.com/gp/product/1609139437?ie=UTF8&tag=radiopaediaor-20&linkCode=as2&camp=1789&creative=9325&creativeASIN=1609139437http://www.amazon.com/gp/product/1609139437?ie=UTF8&tag=radiopaediaor-20&linkCode=as2&camp=1789&creative=9325&creativeASIN=1609139437http://www.amazon.com/gp/product/1609139437?ie=UTF8&tag=radiopaediaor-20&linkCode=as2&camp=1789&creative=9325&creativeASIN=1609139437http://dx.doi.org/10.1148/radiol.2412051952http://dx.doi.org/10.1148/radiol.2412051952http://dx.doi.org/10.1148/radiol.2412051952http://www.ncbi.nlm.nih.gov/pubmed/17057083http://www.ncbi.nlm.nih.gov/pubmed/17057083http://www.ncbi.nlm.nih.gov/pubmed/17057083http://www.ncbi.nlm.nih.gov/pubmed/17057083http://radiology.rsna.org/content/159/1/25.citationhttp://radiology.rsna.org/content/159/1/25.citationhttp://radiology.rsna.org/content/159/1/25.citationhttp://www.ncbi.nlm.nih.gov/pubmed/3952313http://www.ncbi.nlm.nih.gov/pubmed/3952313http://www.ncbi.nlm.nih.gov/pubmed/3952313http://www.ncbi.nlm.nih.gov/pubmed/3952313http://dx.doi.org/10.1148/rg.e17http://dx.doi.org/10.1148/rg.e17http://dx.doi.org/10.1148/rg.e17http://www.ncbi.nlm.nih.gov/pubmed/14610245http://www.ncbi.nlm.nih.gov/pubmed/14610245http://www.ncbi.nlm.nih.gov/pubmed/14610245http://erj.ersjournals.com/cgi/pmidlookup?view=long&pmid=7758551http://erj.ersjournals.com/cgi/pmidlookup?view=long&pmid=7758551http://erj.ersjournals.com/cgi/pmidlookup?view=long&pmid=7758551http://www.ncbi.nlm.nih.gov/pubmed/7758551http://www.ncbi.nlm.nih.gov/pubmed/7758551http://www.ncbi.nlm.nih.gov/pubmed/7758551http://dx.doi.org/10.1177/0218492309104750http://dx.doi.org/10.1177/0218492309104750http://www.ncbi.nlm.nih.gov/pubmed/19643850http://www.ncbi.nlm.nih.gov/pubmed/19643850http://www.ncbi.nlm.nih.gov/pubmed/19643850http://dx.doi.org/10.1148/radiographics.14.2.8190958http://dx.doi.org/10.1148/radiographics.14.2.8190958http://dx.doi.org/10.1148/radiographics.14.2.8190958http://www.ncbi.nlm.nih.gov/pubmed/8190958http://www.ncbi.nlm.nih.gov/pubmed/8190958http://www.ncbi.nlm.nih.gov/pubmed/8190958http://dx.doi.org/10.1148/radiographics.14.2.8190958http://www.ncbi.nlm.nih.gov/pubmed/19643850http://dx.doi.org/10.1177/0218492309104750http://www.ncbi.nlm.nih.gov/pubmed/7758551http://erj.ersjournals.com/cgi/pmidlookup?view=long&pmid=7758551http://www.ncbi.nlm.nih.gov/pubmed/14610245http://dx.doi.org/10.1148/rg.e17http://www.ncbi.nlm.nih.gov/pubmed/3952313http://www.ncbi.nlm.nih.gov/pubmed/3952313http://radiology.rsna.org/content/159/1/25.citationhttp://www.ncbi.nlm.nih.gov/pubmed/17057083http://www.ncbi.nlm.nih.gov/pubmed/17057083http://dx.doi.org/10.1148/radiol.2412051952http://www.amazon.com/gp/product/1609139437?ie=UTF8&tag=radiopaediaor-20&linkCode=as2&camp=1789&creative=9325&creativeASIN=1609139437http://books.google.com/books?vid=ISBN1609139437http://books.google.com/books?vid=ISBN1609139437http://radiopaedia.org/articles/missing?article%5Btitle%5D=unilateral-absence-of-pulmonary-artery-uapahttp://radiopaedia.org/articles/right-middle-lobe-atelectasishttp://radiopaedia.org/articles/pulmonary_sequestrationhttp://radiopaedia.org/articles/missing?article%5Btitle%5D=left-atriumhttp://radiopaedia.org/articles/pulmonary-hypertensionhttp://radiopaedia.org/articles/missing?article%5Btitle%5D=eisenmenger-syndrome8/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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8. Konen E, Raviv-Zilka L, Cohen RA et-al. Congenital pulmonary venolobar syndrome:
spectrum of helical CT findings with emphasis on computerized reformatting.
Radiographics. 2003;23 (5): 1175-84.doi:10.1148/rg.235035004-Pubmed citation
Synonyms & Alternative Spellings
Synonyms or Alternative Spelling Include in Listings?
Pulmonary venolobar syndrome
Congenital pulmonary venolobar syndrome (CVLS)
Scimitar's syndrome
Hypogenetic lung syndrome
http://dx.doi.org/10.1148/rg.235035004http://dx.doi.org/10.1148/rg.235035004http://dx.doi.org/10.1148/rg.235035004http://www.ncbi.nlm.nih.gov/pubmed/12975508http://www.ncbi.nlm.nih.gov/pubmed/12975508http://www.ncbi.nlm.nih.gov/pubmed/12975508http://www.ncbi.nlm.nih.gov/pubmed/12975508http://dx.doi.org/10.1148/rg.2350350048/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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Scimitar Syndrome A tubular
lesion in in the right lower zone with increasing diameter inferiorly.This is classic apperance of the
scimitar syndrome. It can be associated with hypoplasia of the right middle/ lower lobe.
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From the case:Scimitar syndrome
Modality: MRI
http://radiopaedia.org/cases/scimitar-syndrome-3http://radiopaedia.org/cases/scimitar-syndrome-3http://radiopaedia.org/cases/scimitar-syndrome-3http://radiopaedia.org/cases/scimitar-syndrome-38/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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From the case:
Scimitar syndrome
http://radiopaedia.org/cases/scimitar-syndrome-1http://radiopaedia.org/cases/scimitar-syndrome-1http://radiopaedia.org/cases/scimitar-syndrome-18/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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From the case:Scimitar syndrome
http://radiopaedia.org/cases/scimitar-syndrome-1http://radiopaedia.org/cases/scimitar-syndrome-1http://radiopaedia.org/cases/scimitar-syndrome-1http://radiopaedia.org/cases/scimitar-syndrome-18/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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From the case:Scimitar syndrome
Modality: X-ray
http://radiopaedia.org/cases/scimitar-syndrome-8http://radiopaedia.org/cases/scimitar-syndrome-8http://radiopaedia.org/cases/scimitar-syndrome-8http://radiopaedia.org/cases/scimitar-syndrome-88/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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Abnormal curvilnear shadow
overlying the heart in the right hemithorax - characteristic Scimitar finding.From the case:Scimitar
syndrome
Modality: X-ray
http://radiopaedia.org/cases/scimitar-syndrome-6http://radiopaedia.org/cases/scimitar-syndrome-6http://radiopaedia.org/cases/scimitar-syndrome-6http://radiopaedia.org/cases/scimitar-syndrome-6http://radiopaedia.org/cases/scimitar-syndrome-6http://radiopaedia.org/cases/scimitar-syndrome-68/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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From the case:Scimitar syndrome
Modality: CT
http://radiopaedia.org/cases/scimitar-syndrome-7http://radiopaedia.org/cases/scimitar-syndrome-7http://radiopaedia.org/cases/scimitar-syndrome-7http://radiopaedia.org/cases/scimitar-syndrome-78/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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Archery target Archery target
for use in target sign articles. target sign of intussesceptionPermission is granted to copy, distribute
and/or modify this document under the terms of the GNU Free Documentation License, Version 1.2 or
any later version published by the Free Software Foundation; with no Invariant Sections, no Front-Cover
Texts, and no Back-Cover Texts. A copy of the license is included in the section entitled "GNU Free
Documentation License".Original file:
http://commons.wikimedia.org/wiki/File:Archery_target.jpgAuthor: Casito
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From the case:
Bull's eye sign (from cerebral metastasis)
Modality: MRI
http://radiopaedia.org/cases/bulls-eye-sign-from-cerebral-metastasishttp://radiopaedia.org/cases/bulls-eye-sign-from-cerebral-metastasishttp://radiopaedia.org/cases/bulls-eye-sign-from-cerebral-metastasis8/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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From the case:Intussusception
Modality: Ultrasound
http://radiopaedia.org/cases/intussusception-3http://radiopaedia.org/cases/intussusception-3http://radiopaedia.org/cases/intussusception-3http://radiopaedia.org/cases/intussusception-38/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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From the case:Bull's eye sign
Modality: MR
http://radiopaedia.org/cases/bulls-eye-sign-1http://radiopaedia.org/cases/bulls-eye-sign-1http://radiopaedia.org/cases/bulls-eye-sign-1http://radiopaedia.org/cases/bulls-eye-sign-18/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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A
small 'pit' of barium contained within an ulcer cavity in the body of the stomachFrom the case:
Gastric ulcer - a bull's eye
Modality: Fluoroscopy
http://radiopaedia.org/cases/gastric-ulcer-a-bulls-eyehttp://radiopaedia.org/cases/gastric-ulcer-a-bulls-eyehttp://radiopaedia.org/cases/gastric-ulcer-a-bulls-eye8/11/2019 Radiological Signs ( Shnja Radiologjike )-9
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