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Autoimmune sclerosing
pancreatitisSamreen Raza, MD
PGY-3
Autoimmune pancreatitis
• Numerous names• Sclerosis of the pancreas (Sarles, 1961)• Chronic sclerosing pancreatitis• Lymphoplasmacytic sclerosing pancreatitis• Nonalcoholic duct destructive pancreatitis• Sclerosing pancreatitis• Sclerosing pancreaticocholangitis• Autoimmube chronic pancreatitis
• Autoimmune pancreatitis (Yoshida, 1995)
Autoimmune pancreatitis epidemiology• National survey in Japan (2002)• Prevalence – 0.82/100,000
Clinical presentation
• Acute: • Acute/recurrent episodes of pancreatitis - rare• Painless obstructive jaundice (ddx pancreatic cancer)
• Subacute/late: • Persistent pancreatic mass• Atrophic pancreas +/- calcifications• Unexplained steatorrhea