Patient 45 y.o. female with bilateral progressive paraparesis in the last month. No other disease in anamnesis. Brain MR negative
Case n.1Case n.1
RM. Sequenze T1-W without contrast media and T2
T2T2
GradientGradient--ecoeco
T1 T1 ––
coronal coronal without Gdwithout Gd
and T1and T1
axialaxial afterafter
GdGd
Primitive melanocit melanoma.
.
Male.39 y.o. Since 2 months superior arm weakness with increasing pain in the last week.. Brain MR negative.
T1T1
T2T2
T1 +T1 +
GdGd
controllo dopo sette giorni di terapia cortisonica ad alte dosi
T1 +T1 +
GdGd
Primitive Linphoma
Paz. di 46a., female, hypostenia in the last few days
T1 con GdT1 senza Gd T2
T2DP
T2
PtPt 55 y.o55 y.o withwith aa known known hematologic diseasehematologic disease
T1 senza MDCT1 senza MDC
T1 senza MDCT1 senza MDC
Diversi pazienti affetti da “talassemia intermedia”
T1T1
T2T2 T2T2
TC senza MDCTC senza MDC
T1 senza MDCT1 senza MDC
EXTRA-MEDULLARY ERITROPOIESI
CAUSE
••CONGENITAL HEMOGLOBINOPATYCONGENITAL HEMOGLOBINOPATY
intermedia thalassemia MORE FREQUENT (24-65%), sferocitosi, varie anemie emolitiche
•• ACQUIRED PATHOLOGYACQUIRED PATHOLOGY
MIELOFIBROSIS
LEUCEMIE
LINFOMI
• CARCINOMI (LIVER
• FIBROSARCOMI
• PAGET
•RARE • POLICITEMIA
• M. DI GAUCHER
• Cause sconosciute....
LOCATION
• FREQUENT
• PARAVERTEBRALE (soprattutto dorsale)
• SPLEEN
• LIVER
• KIDNEYS
• RARE
• ADRENAL - CUTE /
•LINFONODES – PLEURA – POLMONI -TRACHEA
• ENDOCRANIC
• PERITONEAL / RETRO-PERITONEAL
• MENINGI
• REGIONE SELLARE
• APICE ORBITARIO