Subject Index to Volume 5

Abnormal behavior, 255 abnormal eye movement, 130, 189 abnormal muscle contraction

during sleep, 250 achalasia of the cardia, 239 acid maltase, 246 ACTH, 140, 190, 192, 194,464 acquired in utero, 253 acquired speech disturbance, 194 acute encephalitis, 203, 204 acute encephalopathy, 207 acute hemiplegia, 213,494 acute infantile hemiplegia, 211 acute toxic encephalopathy, 207 action myoclonus, 233 adenosine nucleotides, 375 adrenogenital syndrome, 46 adrenoleukodystrophy, 229 adverse reaction, 193 after-discharge, 138 agenesis of cerebellar vermis, 163 agenesis of corpus callosum, 163 aging, 582 agnosia, 14 Aicardi syndrome, 166 alert, 151 Alexander disease, 216,217 O!-actinin, 115 alpha-pattern coma, 155 amine receptors, 107 AMP deaminase, 241 anosognosia for speech, 180 antiacetylcholine receptor

antibody, 240 anticonvulsant, 142, 143, 188,

193,194,199,202,203 anticonvulsant effect, 195 anti-EBV antibodies, 206 argininemia, 226 arrested hydrocephalus, 131 arterial hypertension, 269 asphyxia, 137, 159,478,529 ataxia, 209 ataxia-telangiectasia, 172 attention deficit disorder, 153 audiogenic seizure rat, 197 auditory brain stem responses,

130,135,136,137,156,157, 194,216,227

auditory development, 136 auditory response, 158 autistic syndrome, 220, 221 autonomic neuropathy, 239 autopsy, 9,192,223 au toradiography, 148 autosomal inheritance, 320

asymmetrical righting reflex, 150

auditory-evoked eyelid micro-vibration, 159

attentional ability, 153 arachnoid cyst, 162 arginase deficiency, 226 arthrogryposis multiplex congenita,

407 axonal degeneration, 172

Bacterial meningitis, 185,210, 417

basal ganglia calcification, 252 basilar artery occlusion, 577 behavioral audiometry, 157 behavioral states, 152,286 benign epilepsy of childhood with

rolandic discharges (BECRD), 183

benzodiazepines, 141,183, 196 benzodiazepine receptors, 197 j3-galactosidase, 233 j3-galactosidase/neuraminidase

deficiency, 233 6j3-hydroxycortisol, 203 bicaudate CVI, 220 bifrontal CVI, 220 bifrontal extracerebrallow density

area, 160 bifrontal fluid collection area, 173 bifrontotemporal peripheral low

density area, 160 bilaterally synchronous 34 Hz

spike-and-wave activity, 183 bile, 232 biopsy studies, 205,229,230,245 blinking, 278 blink reflex, 474 blood-brain barrier, 146 blood flow velocity, 529 blood level monitoring, 144 blood transfusion, 205 body movement, 151,154 borderline child, 128 bottle feeding, 152 brain amino acids, 195 brain atrophy, 162, 192,255 brain biopsy, 205 brain catecholamine, 195 brain CT scan, 46, 155, 165,204,

211,223 brain damaged child, 127 brain development, 145,147 brain dysfunction, 488 brain parasites, 269

brainstem encephalitis, 205,211 brainstem function, 156, 157 brain stem lesion pattern, 137 brain stem response audiometry,

130 brainstem reticular formation, 474 brain tumor, 214 branchial fistulas, 41 breast feeding, 152 bronchial asthma, 219 Burdon's test, 153

Caffeine, 395 calcification, 191,248,252,323 calcium-dependent Ach release,

239 calcium mobilization, 511 Canavan disease, 217 CANP, 115 carbamazepine, 144, 196 cardiac failure, 251 carnitine, 198 carrier detection, 244 catalase, 228 catch-up growth, 148 catecholaminergic system, 191 cathepsin B, 233 cavum septi pellucidi, 163 cavum Vergae, 163 center of gravity, 173 cell mediated immunity, 29 central cerebral discoordination

175,176,311 cerebellar cyst, 163 cerebellar hypoplasia, 41,503 cerebellum, 148 cerebral atrophy, 162, 192,255 cerebral blood flow, 36,58,525· cerebral cysticerosis, 269 cerebral coordination disturbance

(CCD), 175,176,311 cerebral infarction, 209, 213 cerebral motor disturbance, 173 cerebral palsy, 1,127,137,139,

157,173,174,176,177,179, 189,311,478

cerebral perfusion pressure, 478 cerebrovascular disease in childhood

211,363 cerebro-oculo-muscular dystrophy

302 cerebrospinal fluid, 131,206,214,

221,224,234,235,357,464, 483,488,509

cerebrum, 204, 307, 397 ceroid lipofuscinosis, 228

Subject index 595

cervical spinal cord tumor, 236 "C-glucose, 161 childhood epilepsy, 188 childhood myathenia gravis, 240 childhood type acid maltase

deficiency, 246 child neurology, 135 chromosomal aberration, 129 chronic headache, 221 chronic lung disorders, 222 circadian rhythm, 220 circulating immune complex

201 clumsy children, 15, 128 CNP activities, 145 "CO., 161 Cockayne syndrome, 171 collagen, 170,450 coma, 155,256 communicating hydrocephalus, 41 compensated hydrocephalus, 131 computed tomographic metrizamide

myelography, 236 computed tomography, 14, 160,

176,192,207,214,221,414, 494,564

confronting cisternae, 549 congenital contractures, 407 congenital fiber type disproportion,

252 congenital intraspinal lipoma, 133 congenital malabsorption of folate,

234 congenital malformation, 41,148,

164, 166 congenital muscular dystrophy,

165,243,244,248,292,302 congenital myopathy, 53, 116,

250,252 congenital nystagmus, 130 congenital spinal anomaly, 167 consciousness disturbance, 155,

159,256 continuous muscle contraction,

250 contralateral stimulation, 156 conus medullaris, 235 convulsions in early infancy, 320 convulsive disorders, 184, 185,

187,320,469 copper, 232 copper-associated protein, 231 copper metabolism, 533 corpus callosum, 166 cortical atrophy, 46 corticosteroid hormone, 218 CPK, 247 creatine, 242 crippled children's hospital, 177 crying, 151 CSF dynamics, 131 CSF pleocytosis, 211 CSF pressure, 214 CT scan, 48, 160, 161, 162, 166,

170,172,173,174,175,177, 179,187,194,204,206,209, 212,216,217,218,220,229, 269,323,327

cytomegalovirus encephalitis, 204, 327

cytochemistry, 146 cytochrome c oxidase, 232,533 cytochrome c oxidase deficiency,

231 cytolysosome, 146 cytomegalic inclusion encephalitis,

204,327 cytoplasmic body, 315 cytosine arabinoside, 147,148

Damped rotation test, 209 Dandy-Walker cyst, 133 dantrolene sodium, 242 DAOD, 164 deafness, 130,209,217 delayed motor development, 311 demyelination, 230 dendrites, 145 denervated muscle, 241 dermatomyositis, 53,248 developmental apraxia, 14 developmental disability, 128, 179 developmental disturbance, 127 developmental profile, 168 developmental retardation, 250 developmental word deafness, 180 developmental screening, 127 diazepam, 183,196 diencephalic cyst, 163 diffuse spike-wave burst, 182 dilated pupils, 239 dilatated ventricles, 134 dimefline, 254, 568 dipropyl acetate, 143, 197, 198,

199,334 discontinuation of antiepileptics,

188 DN-1417 (TRH analog), 421 DNA content, 145 Doppler flowmeter, 525 Doppler ultrasound method, 179,

363 Down syndrome, 168 D-penicillamine, 48, 232 driver's license, 187 DTVP, 181 Duchenne muscular dystrophy,

241,242,244,511 dysphagia, 180 dysraphic states, 167 dystrophic chicken, 241

Eearly infantile autism, 220, 221 EEG, 138, 153, 154, 155, 162,

172,177,187,188,190,203, 211,224,226,234,256

EEG topography, 162 electromyography, 245

596 Brian & Development, Vot5, No 6,1983

electroretinogram, 225 El mouse, 149 emergency service, 185 emergency treatment, 185 emotional disorders, 255 encephalitis, 103,203,204,205,

206,211,327,564 encephalopathy, 189,199,207,

208,222,324 enzyme replacement therapy, 226,

228 epidemiology, 181 epidemic myalgia, 249 epilepsy, 100,108,140,142,143,

148,166,181,182,187,188, 193,196,198,200,202,203, 238,320,357,469,509

epileptic discharge, 20, 186 epileptic encephalopathy, 194 epileptic seizures, 141 episodic tachypnea and apnea, 169 Epstein-Barr virus (EBV), 206 erythrophagocytic lymphohistio-

cytosis, 323 ethanol, 549 external hydrocephalus, 13 2 eye movement disturbances, 41,

278

Facial expressions, 278 facial palsy, 371 facio-scapulo-humeral muscular

dystrophy, 243 failure to thrive, 129 falx image, 161 famili al macrocephaly, 166 far field potential, 390 fatal hepatitis, 199 febrile convulsion, 181,182,183,

185,196,357,469 fetal alcohol syndrome (F AS), 549 fibroxanthoma, 236 Fischer syndrome, 221 flash stimuli, 474

• floppy infant, 250 folinic acid, 234 free-field observation, 219 Fukuyama type congenital muscular

dystrophy, 165,243,244,248, 292,302

GABA (gamma-aminobutyric acid), 100,233,235

GAD, 149 gamma-CBF, 147 gammaglobulin therapy, 193 gas-liquid chromatography, 582 gastro-enteritis, 185 Gaucher disease, 227 generation time of the granular

cells, 148 GF AP immunoperoxidase stain,

163,216,244 glial proliferation, 244

globus pallidus, 223 glutamic acid decarboxylase, 234,

483,488 glutamine, 509 glycine, 242 glycogen storage disease, 246, 247 GM1-gangliosidosis, 229 GM2-gangliosidosis, 227 grand mal epilepsy, 186 granular cell number, 148 granuloma, 499 growth, 474 growth hormone, 222 'Y-GTP isozyme, 203 Guillain-Barre syndrome, 237

Haloperidol poisoning, 255 handedness, 149 HDL-cholesterol, 201 head circumference, 166 headache, 221 health examination, 181 heart rate, 154 hemihypotrophy, 407 hemiplegia, 212,371 hemoglobin AI, 224 hemorrhagic pancreatitis, 208 hepatic cytochrome P-450, 203 hepatitis, 199 hereditary mouse, 238 herpes simplex encephalitis, 204,

206,327 high fat diet, 381 high risk baby, 1,158 hippocampus, 549 hippuric acid, 555 histochemistry, 245 histogenesis, 163 holoprosencephaly, 163 homocarnosine, 464, 509 homovanillic acid, 235 horseradish peroxidase, 146 HPLC, 450 human fetal muscle, 245 hump, 162 hydranencephaly, 164 hydrocephalus, 41,131,132,133,

134,147,164,210,216,252, 255,414

hydroxy-proline, 450 5-hydroxyindoleacetic acid, 235 hyperaminoacidemia, 206, 207 hyperammonemia, 198,199,226,

334 hyperargininemia, 555 hypergonadotropic hypogonadism,

568 hyperkinetic children, 219 hyperosmolality, 146 hypodense area, 48,206,564 hypoglycemic episode, 224 hypoxic encephalopathy, 222 hypoxic-ischemic encephalopathy,

189

14 and 6 Hz positive spikes, 153

I -cell disease, 230 ictal CBF, 58 ictal EEG, 141 idiopathic intestinal pseudo-

obstruction (lIP), 225 IgM, 164 immune defects, 29 immunoglobulin, 199 inborn errors of metabolism, 129 induced micro seizures, 141 infant audiometry, 130 infantile convulsion, 184, 185,

320,469 infantile diarrhea, 184 infantile Gaucher disease, 227 infantile intractable epilepsy, 100 infantile opsoclonus polymyoclonia

syndrome, 218 infantile polymyositis, 53 infantile spasms, 137, 140, 189,

190,191,192,193,464 influenza A virus, 564 interferon, 205 internal carotid blood flow velocity,

179,363 intracranial calcifications, 191,

248, 252, 323 intracranial germinoma, 215 . intracranial hemorrhage, 159, 161,

189,478 intracranial mass, 223 intracranial pressure, 255, 478 intractable epilepsies, 36,100,

195,201,375,421 intrauterine infection, 164,248 intra-ventricular hemorrhage, 189 involuntary movement, 217 ipsilateral stimulation, 156 IQ, 133 Isaac syndrome, 250 isoniazid, 233

Juvenile diabetics, 224 juvenile metachromatic leuko-

dystrophy, 228 juvenile myasthenia gravis, 240 Joubert syndrome, 169

Kawasaki disease, 224,371 keratan sulfate, 227 ketogenic diet, 100,195,375 kinematic analysis, 174

Lactic acidemia, 252 lacunar infarct, 212,494 language acquirement, 180 language delay, 128 LCAT activity, 201 Leigh's encephalomyelopathy, 231 Lennox-Gastaut syndrome, 140,

190,193 leu com ala cia, 222

leukemia, 223 leukodystrophy, 216,217,228 leukopheresis (leucocytes infusion),

228 lipid peroxide, 202,457 lipopigment, 228 lissencephaly, 163,165,302 liver damage, 334 long-term prognosis, 184,215,469 low density areas, 48, 206 low IgA, 196 low vitamin A diet, 228 low voltage activity, 162 lysosomal hydrolase, 230

Macrocephaly, 166 malformation, 148, 164, 166 malignant hyperthermia, 243 marriage, 187 mass-screening, 129 maturational defect, 236 maximal electroconvulsive

threshold, 375 McArdle disease, 247 measles, 29 mechanical ventilation, 251 megacisterna magna, 41 meningitis, 185,209,210,357,

414,417,509 Menkes kinky hair disease, 232,

533 mental deterioration, 168, 190 mental disorders, 139 mental retardation, 41,173,177,

238,302 mesial temporal structure, 221 metabolic myopathy, 116 metachromatic leukodystrophy,

228 metallothionein, 231 methylephedrine, 239 methylphenidate, 219 3-methoxy4-hydroxyphenylglycol,

235 metrizamide, 167 microcephaly, 147,457 microdensitometry, 142 microsome test, 201 midbrain reticular formation, 159 middle chain triglyceride, 375 migraine, 221 Millard-Gubler syndrome, 139 minimal brain dysfunction, 181 minimal change muscle pathology,

253 minor abnormal neurological signs,

128 mitochondrial abnormality, 250 mitochondrial encephalomyopathy,

252 MLF, 130 Mobius syndrome, 168 monitoring of anticonvulsants, 143

SubjeCt index 597

monitoring of intracranial pressure, 255

monoamine metabolism, 200 monopharmacy, 140,143,144 motor development, 152 motor disturbance, 173, 220 moxalactam, 417 multiple-handicapped children,

178 multiple sulfatase deficiency, 230 multivariate analysis, 1 mumps, 208 muscular CT-scanning, 407 muscular dystrophy in young girls,

244 muscle biopsy, 243, 248 muscle contraction headache, 221 muscle fiber differentiation, 572 muscle histochemistry, 249 muscle hypotonia, 250 muscle maturation, 253 muscle phosphorylase, 247 myathenia gravis, 239, 240 myelination, 145 myelin protein components, 145 myelography, 167 myeloradiculo-neuritis, 237 myoclonic epilepsy, 186,252 myoclonic seizure, 193 myoclonus, 218,233 myogenic changes, 243 myoglobin, 242 myokymia, 250 myopathy, 53, 116,248,250,

252,253 myotonia conge nita, 249

Nasopharyngeal carcinoma, 206 N-desmethyldiazepam, 183 nemaline bodies, 251 nemaline myopathy, 53,251 neocortex, 582 neonatal asphyxia, 137, 145, 159 neonatal behavior, 151,158 neonatal convulsions, 197, 320,

541 neonatal hyperbilirubinemia, 137 neonatal hypoxia, 145,159 nerve cell size, 149 nerve fiber density, 237 nerve fiber diameter, 237 neuraminidase, 233 neuroblastoma, 218 neurocutaneous melanosis, 172 neurocutaneous syndrome, 503 neurogenic changes, 243 neuromuscular diseases, 245 neuropathology, 192,323 neuropathy, 238,239 neurophysiological maturation,

139 neuropsychological study, 190 neurotransmitter, 254 newborn babies' sleep, 154

NG-dimethylarginine, 242 non-autoimmune myasthenia gravis,

240 normal pressure hydrocephalus,

255 nucleic acids, 397,457 nutritional rehabilitation, 148 nystagmus, 130

Occlusion of bilateral internal carotid artery, 213

Ondine's curse, 254,568 opsoclonus, 218 optimum serum level, 143 organoid nevus, 503 orientating response, 158 orotic acid, 555 orthostatic dysregulation, 225

Paradoxic release, 222 paralysis, 212 parent-child relation, 219 parenteral moxalactam, 417 PDC deficiency, 231 pentetrazol, 195 perception, 181 perinatal asphyxia, 137,145,159 periodic discharge, 206 peroneal muscular atrophy, 238 peroxidase, 228 persistent head turning, 149 personality, 20 petit mal seizure, 58 pharmacokinetics, 197 phenylacetic acid, 555 phenylalanine restricted diet, 226 phenylketonuria, 226 phenytoin, 142,144,203 photoconvulsive response, 186 photo-evoked eyelid microvibration,

159,474 photopalpebral reflex, 159 photosensitive epilepsy, 138 photosensitive myoclonic epilepsy,

186 pituitary dysfunction, 217 plagiocephaly, 149 platelet dysfunction, 198 polygraphic sleep study, 191 polymicrogyria, 165,302 polymyositis, 53,247,248 polyneuritis, 237 polysomnography, 168, 169, 286 porencephaly, 162 positron emission computed

tomography, 161 postencephalitic epilepsy, 203 posterior fossa lesions, 216 postural development, 152 postural plagiocephaly, 149 postural reactions, 150, 173 postural reflexes, 311 posture, 151 power spectrum, 194

598 Brian & Development, Vol 5, No 6, 1983

PPRF, 130 Prader-Willi syndrome, 169 precocious puberty, 215,414 pregnancy, 397 primary generalized epilepsy, 182 prognosis, 182, 292 prognosis of epileptic seizures, 141 prognostic factors, 469 progressive muscular dystrophy,

115,165,241,242,243,244, 248,292,302,511

progressive myoclonus epilepsy, 233

proline, 450 prostaglandin F, 357 psychogeneity, 108 psychogenic overlay, 108 psychometry, 181 psychomotor development, 225 psychosomatic disease, 219 pull-to-sitting, 174 pulsatility index, 525,529 purulent meningitis, 209 putamen, 564 pyridoxal phosphate, 193 pyruvate decarboxylase deficiency,

381 pyruvate dehydrogenase deficiency,

572

Radiation, 214 radiation therapy, 215 Ramsay-Hunt syndrome, 138 raphe nucleus, 220 receptor, 107, 197,240 rectal administration, 196 recurrent polyneuritis, 237 rehabilitation, 180 REM, 255 repiratory failure, 251, 254 respiration, 168,286 retardation, 441 Reye syndrome, 199,207,208,

324 RFP, 210 rickets, 142 righting reflex acting on the head,

150 risk factor, 1,168,175 RNA, 549 rods, 53 rolandic discharges, 183 rolling over, 150 Rosenthal fiber, 216 Rotavirus, 185

Salivary IgA, 142 satellite cell population, 236 school education for handicapped

children, 178 schizencephaly, 165 sclerosing panencephalitis, 20, 157 screening, 129 seizure activity, 162

seizure control, 188 seizures, 197,212 seizures induced by photic

stimulation, 186 seizure types, 170 sensory neuropathy, 238 sensory pathway, 158 septal glioma, 215 serum alkaline phosphatase, 202 serum bile acids, 511 serum calcium, 202 serum IgA, 142,193 serum Mg, 200 serum phosphate, 202 serum Zn, 200 sex chromatin, 129 sex difference, 136, 150 short latency somatosensory

evoked potentials, 139, 158, 390

shuffling, 167 SIADH, 223 sign language, 180 skin biopsy, 229 skinned fiber, 243 sleep, 153, 154, 191 sleep apnea, 151 sleep polygraph, 168, 169, 286 sleep posture, 286 sleep spindle, 154 sleep states, 151 slit like ventricle, 134 slow wave activity, 162 sodium valproate, 140, 143, 144,

197,198,199,200,334 sodium benzoate, 555 speech disturbance, 128, 180, 194 speech therapy, 180 spina bifida occulta, 167 spinal cord tumor, 133, 167,235,

236 spinal lipoma, 133, 167 spindle coma, 155 spindle lazy, 162

spastic diplegia, 174, 175 spastic hemiplegia, 177 spastic paraplegia, 238 SSPE, 20, 157 STA-MCA anastomosis, 213 steroid therapy, 240 striatum, 218 sub arachnoidal dilatation, 160 subdural hygroma, 162,214 subdural-peritoneal shunt, 499 subdural effusion, 160,499 subdural hematoma, 162,214 subdural tapping, 160 subependymal haemorrhage, 9 sucrose loading, 230 superoxide dismutase, 228,457 supraoptic nucleus, 223 suprasellar lesions, 216 sural nerves, 172,237 sural nerve biopsy, 230 susceptibility to infection, 142 symmetrical low density areas, 218

Terminal dural sac, 235 theophylline, 145 THF, 29 thiamin, 146 Thomsen disease, 249 thrombocytopenia, 197 thymidine kinase, 397 thyroid test, 201 total parenteral nutrition (TPN),

225 traction response, 174 TRH, 222, 254, 256 TRH analog, 195 tube feeding, 180 tuberculous meningitis, 210 tuberous sclerosis, 46, 170,215,

450 tubular structure, 248 type 2B fiber deficiency, 246 type 2C fibers, 236,238,572 type 1 muscle fiber atrophy, 250

Ultrastructure, 204,229,327 unconsciousness, 155, 159,256 unilateral seizures, 187 urokinase, 213 UV sensitivity, 171

Valproate (valproic acid), 100, 140, 143, 144, 197, 198, 199, 200,334

varicella, 212,494 varicella encephalitis, 206 vermian agenesis, 169 vincristine, 223 viral myositis, 249 visual evoked potential, 138,194,

225 visual following test, 173 vitamin A, 228 vitamin B6, 233 vitamin B2-butyrate, 202 vitamin E, 202 Vojta's physiotherapy, 173,174,

175,176,311 von Recklinghausen disease, 170

Walking ability, 174,175 water content, 582 Werdnig-Hoffmann disease, 238,

315 West syndrome, 137,140,189,

190,191,193,464 white matter, 191 widely open fontanelles, 134 Wilson disease, 48,231,232

Xeroderma pigmentosum, 171 X-irradiation, 457 X-linked inheritance, 41

Y-G personality test, 188

Zellweger syndrome, 165 zinc, 549

Subject index 599